English Translation, Synonyms, Definitions and Usage Examples of Spanish Word ‘enfermedad de Degos’. Meanings of “enfermedad de degos” in English Spanish Dictionary: 1 result(s) Meanings of “enfermedad de degos” with other terms in English Spanish. Me llamo Loli tengo 37 años y vivo en Madrid y me diagnoticaron la enfermedad de Degos en despues de que perdiera la vision del ojo.
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Face, scalp, palms of snfermedad and soles of feet are rarely involved. Disease definition Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim.
Prognosis Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions. Differential diagnosis The histology of early lesions resembles cutaneous lupus erythematosus re this term. Hypotheses implicating vasculitis, coagulopathy or a primary dysfunction of endothelial cells have been proposed. All articles are subjected to a rigorous process of revision in pairs, and careful editing for literary and scientific style.
Diagnosis is based primarily on the cutaneous clinical picture that is nearly pathognomonic. Diagnostic methods Enfermexad is based primarily on the cutaneous clinical picture that is nearly pathognomonic. More developed lesions show prominent changes in the dermoepidermal junction, with atrophy of the epidermis and an area of sclerosis in the papillary dermis. From Monday to Friday from 9 a. If you are a member of the AEDV: Over several days, the center of the lesions sinks and ddgos a characteristic morphology: For all other comments, please send your remarks via contact us.
This condition is chronic and lesions persist over years, often throughout life. Malignant atrophic papulosis MAP is a rare, chronic, thrombo-obliterative vasculopathy characterized by papular skin lesions with central porcelain-white atrophy and a surrounding teleangiectatic rim. Previous article Next article. Pemphigus Vegetans in the Inguinal Folds. A clinical inspection of the skin should be combined with additional examinations including brain magnetic resonance tomography, gastroscopy, colonoscopy, X-ray of the chest and abdominal ultrasound, in order to assess the long-term prognosis.
CiteScore measures average citations received per document published. Continuing navigation will be considered as acceptance of this use. Clinical description MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, enfermedaad on the trunk and the enfetmedad extremities.
You can change the settings degoos obtain more information by clicking here. Go to the members area of the website of the AEDV, https: MAP onset occurs in adults aged with skin lesions that appear initially as small erythematous papules, predominantly on the trunk and the upper extremities.
Management and treatment Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
The material is in no way intended to replace professional medical care by a qualified specialist and should not be used as a basis for diagnosis or treatment. Additional information Further information on this disease Classification enffermedad 3 Gene s 0 Clinical signs and symptoms Publications in Fe Other website s 7.
enfermedad de Degos – English Translation – Word Magic Spanish-English Dictionary
Etiology The etiopathogenesis of the disease remains unknown. Idiopathic, monosymptomatic, cutaneous presentations are benign, however, systemic manifestations can develop years after the occurrence of skin lesions.
Ocular involvement, which affects the eyelids, conjuctiva, retina, sclera and the choroid plexus, as well as the development of diplopia and ophthalmoplegia as secondary side effects of the neurologic involvementhas also been described. Specialised Social Services Eurordis directory. It may more rarely manifest as pericarditis or in other organs such as the lungs, presenting as pleuritis.
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The documents contained in this web site are presented for information purposes only. Si continua navegando, consideramos que acepta su uso. Therapeutic efforts with anticoagulants and compounds that facilitate blood perfusion, such as acetylosalicylic acid, pentoxifylline, dipyridamole, ticlodipine and heparin have achieved a partial regression of skin lesions in some individual cases.
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This item has received. Many patients have been reported to have defects in degoos coagulation. Genetic counseling A genetic predisposition with an autosomal dominant trait has been suggested.
Later a wedge-shaped connective tissue necrosis in the deep dermis, due to a thrombotic occlusion of the small arteries and sparse lymphocytes, occurs. Read this article in English. Systemic lesions may affect the gastrointestinal tract and the central nervous system CNS and are potentially lethal. To improve our services and products, we use “cookies” own or third parties authorized to show advertising related to client preferences through the analyses of navigation customer behavior.
As all patients may potentially develop the systemic, life-threatening variant, an annual follow-up is mandatory. Health care resources for this disease Expert centres 69 Diagnostic tests 0 Patient organisations 21 Orphan drug s 0. Only comments seeking to improve the quality and accuracy of information on the Orphanet website are accepted.